Immunoglobulin resistance in Kawasaki disease with chronic granulomatous disease
نویسندگان
چکیده
منابع مشابه
Predictors of Intravenous Immunoglobulin (IVIG) Resistance in Children with Kawasaki Disease in Calabria Region, Italy
Background Kawasaki disease (KD) is the second most common childhood vasculitis and one of the main causes of acquired heart disease in children. Recent work focuses on the early diagnostic importance of those risk factors that indicate resistance to intravenous immunoglobulin (IVIG) treatment. The objectives of this study were to identify clinical, laboratory and/or instrumental factors that c...
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Background Kawasaki Disease (KD) is a vasculitis with multi-organ involvementof unknown etiology; it is the most common cause of pediatric-heart diseases in developed countries. Treatment with Intravenous Immunoglobulin (IVIG) prevents coronary artery lesions; although there are some IVIG-resistant cases, combination therapy with corticosteroids and IVIG is one of the recommendations for treatm...
متن کاملFactors Predicting Resistance to Intravenous Immunoglobulin and Coronary Complications in Kawasaki Disease: IVIG Resistance in Kawasaki Disease
https://e-kcj.org Downie et al.1) defined intravenous immunoglobulin (IVIG) resistance in patients with Kawasaki disease (KD) as any patient who receives a second dose of IVIG and had a fever (body temperature [BT] >38.0°C) since finishing the first IVIG dose (2 g/kg). In addition, patients who do not respond to IVIG (BT ≥37.5°C more than 24 hours after the end of IVIG infusion) seem to develop...
متن کاملintravenous immunoglobulin resistant kawasaki disease
abstract kawasaki disease is a systemic vasculitis that mainly affects younger children. although the definite cause still remains unknown but the clinical and epidemiologic findings discuss an infectious cause. the prevalence of incomplete kawasaki disease reported 15 to 36.2%, and it is more frequent in the extremes of the age spectrum. non delayed treatment of disease should be initiated bec...
متن کاملChronic Granulomatous Disease, Case Report and Review of Literature
Chronic granulomatous disease (CGD) is a rare inherited disorder characterized by inability of phagocytes to generate oxygen radicals needed for intracellular killing of phagocytic microorganisms. We report a 2.5-year-old Iranian female with multiple liver abscesses. She was admitted in surgical ward because of abdominal pain and fever for one month duration that had no response to conventio...
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ژورنال
عنوان ژورنال: Pediatrics International
سال: 2012
ISSN: 1328-8067
DOI: 10.1111/j.1442-200x.2011.03523.x